Trevor disease, also known as dysplasia epiphysialis hemimelica (DEH) is a rare non-hereditary disease affecting the epiphyses of long bones. Histologically, it resembles osteochondromal tissue. Described incidence rate of the disease is 1:1000000, with some authors claiming higher incidence rate in reality due to probably misdiagnosed cases classified as osteochondromas or other similar entities. It is considered a disease of pediatric age population, even though there are sporadic cases of the disease among adults. The main pathological finding in Trevor disease is a painless bone growth affecting a part of the joint, localized along the epiphysis of one or both articular bones. The growth is commonly found in the ankle, the knee or the hip. In some patients, multiple bone growths are present, either along the same or different limbs. Currently, there are no known envirnomental and genetic factors with measured parameters in Trevor disease being completely equal to the values found in healthy tissue. There are no described cases of malignant alteration in the literature. Diagnostic-wise, it is crucial to look for the signs of Trevor disease – asymmetry, impaired mobility and joint deformity. After finding those signs, one or more radiology tehniques are used with the most useful being x-ray, computerized tomography and magnetic resonance imaging. After the lesion is visualized, a thearapeutic approach is chosen, either conservative or surgical, depending on both radiological and clincal findings. With early diagnosis and treatment it is possible to avoid complications like disability caused by impaired mobility of the joint or osteoarthritis. Recovery after the treatment is relatively fast, with one of the described cases stating only 28 days. Considering the pediatric age of the affected, plasticity of the skeletal system greatly contributes to the good results and fast recovery time.