Autoimmune hepatitis is a chronic liver disease of unknown etiology characterized by hepatocellular inflammation, circulating autoantibodies and increased level od immunoglobulin G. There are two main types of AIH in children classified by seropositivity – AIH type 1 (ANA and SMA antibodies positive) and AIH type 2 (anti LKM1 autoantibodies positive). Although the cause of AIH is uknown, immunosupresive treatment is highly efficient and it should start immediately concerning the tendency of AIH for disease progression. Besides AIH there are two more liver autoimmune diseases: overlap syndromes and post-transplant AIH de novo sharing a lot with AIH. Clinical presentation is variable, as I presented in case reports of three patients, which often makes the diagnosis a real challenge. Our understanding of autoimmune diseases has started in the second half of the 20th century, but their characteristics are not yet fully aprehended, so they are a fruitful field for reasearch, making progress and improvement. Our treatment goals are lack of inflammation, symptoms withdrawal, clinical remission and healthy liver or at least good quality of life with minor disease presence. Cirrhosis at the presentation is not an ominous sign regarding natural history of the disease (almost 40-80% of children have cirrhosis according to the initially obtained liver biopsy tissues). Mortality is very low, and majority of patients enjoy almost healthy and productive life with the disease.