Behçet's disease (BD) is a systemic disease described as a vasculitis with autoimmune and autoinflammatory characteristics. HLA-B51 is mentioned as one of the main etiopathogenetic factors and polymorphisms of other genes are mentioned as possible additional factors.The disease is most common on the "Silk Road", and Turkey stands out as the country with the highest prevalence. BD is divided into paediatric BD, with peak onset around 12 years, and BD in adults, where the symptoms appear in the late twenties. Various systems are affected, but it is most often presented as mucocutaneous lesions, on the mucous membranes as recurrent ulcerations, and on the skin in the form of papulopustules or erythema nodosum. In addition, the joints are also affected, most often as arthritis, and the eyes, as uveitis. Treatment is usually based on the EULAR guidelines. This paper presents a patient diagnosed with juvenile BD, whose symptoms appeared at the age of 11. She initially presented with impaired vision that was diagnosed as uveitis, with no other symptoms that would suggest a systemic, immune disease. During evaluation for uveitis, it was discovered that the girl carries the HLA-B51 gene, and over time she developed other symptoms and signs, such as oral ulcerations and arthritis, which would later point to BD. She was diagnosed with BD almost 2 years after the first symptom appeared. The patient was treated with corticosteroids, immunosuppressants and biological therapy. She also developed many complications of the disease, which were successfully cured, and due to the side effects of the treatment, a change of therapy was necessary.